Surgical Intervention and Management of Nursing Care in Paediatric Patients with DiGeorge Syndrome

OpenAlex İngilizce

DiGeorge Syndrome (22q11.2 deletion syndrome) is a genetic disorder affecting multiple organ systems including cardiovascular anomalies, immune deficiencies and developmental delays. Surgical interventions, especially cardiac surgeries, are frequently required in paediatric patients with this syndrome and the importance of a multidisciplinary approach in these processes emerges. In this article, the management of surgical processes in children with DiGeorge Syndrome and the role of nursing care in these processes were examined. The article focuses on critical care areas such as nutrition, immune prophylaxis and infection risk management, as well as the roles of nurses before and after surgery. In addition, the monitoring of complications that may develop due to the characteristics of the syndrome and proactive nursing interventions for these complications are detailed. It is emphasised that nurses, as part of the multidisciplinary team, have a critical role to improve the quality of life of patients and their families, prevent complications and optimise the treatment process. In conclusion, adopting a multidisciplinary approach in the surgical interventions and care processes of paediatric patients with DiGeorge Syndrome is vital in improving patient outcomes and reducing the risk of complications.